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KMID : 1161920140110020115
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Journal of Medicine and Life Science
2014 Volume.11 No. 2 p.115 ~ p.117
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A case of unilateral cochlear nerve deficiency with congenital hearing loss
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Jang Han-Bin
Kim Dong-Young
Song Chan-Il
Kim Se-Hyung
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Abstract
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The narrow bony cochlear nerve canal in high resolution temporal bone computed tomography (TBCT) is frequently found in patients of congenital sensorineural hearing loss. But this bony structural anomaly could not conclude the functional outcome of cochlear nerve. Here we present a case of a 10-month-old girl having unilateral narrow bony cochlear nerve canals. In internal auditory magnetic resonance imaging (IAC MRI), the right cochlear nerve was not identified to be intact. Moreover, acoustic brainstem response threshold and automated acoustic brainstem response revealed nearly deaf hearing threshold. Therefore we suggest that congenital hearing loss patients take TBCT and IAC MRI to rule out the narrow bony cochlear nerve canal.
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KEYWORD
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cochlear nerve deficiency, magnetic resonance imaging, sensorineural hearing loss, unilateral hearing loss
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